Back to results

Record detail

One row in GLEAM-DB is one paper (PubMed) × one query variant. This page shows structured labels and provenance for that record, not a final variant classification.

Record identity

Record ID
96e1453f62d9400cd5dc768f
Release version
webdb_threshold_completion_missing10_20260508
PMID
38515655 PubMed
Title
A novel mutation in GTPBP3 causes combined oxidative phosphorylation deficiency 23 by affecting pre-mRNA splicing.
Journal
Heliyon
Year
2024
DOI
10.1016/j.heliyon.2024.e27199
PMC
PMC10955198 PMC

Variant information

This section prioritizes normalized variant expressions where available. Non-standard source strings are not shown as canonical HGVS.

Gene
GTPBP3
Query variant
NM_032620.4:c.836C>T
Normalized c.HGVS
c.836C>T
Normalized p.HGVS
p.(Pro279Leu)
Representative genomic HGVS
CM000681.1:g.17450270C>T
Genomic HGVS aliases
CM000681.1:g.17450270C>T; CM000681.2:g.17339461C>T; NC_000019.10:g.17339461C>T; NC_000019.8:g.17311270C>T; NC_000019.9:g.17450270C>T; NG_027824.1:g.9480C>T

CoGenEx-PM3 evidence

Evidence status is assigned at the PMID × variant level and should not be interpreted as a final variant-level pathogenicity classification.

Evidence status
Phase-unconfirmed biallelic evidence
Query-evidence confidence
Needs review
Llm Review Not Conclusive For Removal
Phase-confirmed PM3 evidence
No
Phase-unconfirmed biallelic evidence
Yes
Other patient-level evidence
No
PM3 context
Homozygous for query variant
PM3 evidence items
1
Allelic configuration type
Homozygous evidence

No retained PM3 partner variant was recorded for this PMID × variant pair.

Candidate context and target validation

Candidate context windows are places selected for audit because the query or its aliases may be relevant. They are not the same as a validated match to the target c.HGVS or p.HGVS expression.

Candidate context
Candidate context retained: 1 text window and 1 table window
Context status
Found in final retained audit context
Text candidate windows
1
Table candidate windows
1
Target c.HGVS validated
Yes
Target p.HGVS validated
Yes
Target validation
Target variant matched with phase-unconfirmed biallelic evidence

Source provenance

Reviewed source
Supplementary material
Supplement used by audit
Yes
Supplement available
Yes
Reviewed document format
NXML/JATS full text
Evidence context scope
Supplement-focused audit context
Evidence location
Supp

Source links and copyright boundary

Use the PMID, PMC and DOI links above to inspect the source publication where access is permitted. GLEAM-DB redistributes structured metadata, evidence labels and provenance fields only; it does not redistribute copyrighted full text, supplementary tables, copied source tables, long evidence contexts, raw source documents, raw LLM outputs or internal processing logs.

Help improve this record