Search GLEAM-DB / CoGenEx-PM3

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Input query
Recognized gene
GBA1
Normalized c.HGVS
c.1043C>G, c.1043C>T, c.1103G>A, c.1200G>A, c.1279G>A and 14 more
Normalized p.HGVS
p.(=), p.(Ala348Gly), p.(Ala348Val), p.(Arg301His), p.(Arg368His) and 14 more
Matching records
127
PM3-positive records
16

Results are ordered by PM3-relevant evidence first. Reviewed source only indicates whether main text, supplementary material, or both were reviewed; it is not the evidence conclusion.

Download current query results as TSV
Gene Variant Evidence PM3 context Publication Reviewed source Actions
GBA1 NM_000157.4:c.1279G>A Phase-unconfirmed biallelic evidence
High confidence
Homozygous for query variant
context: Homozygous evidence
41890995
The GBA1 p.E427K (p.E388K) Variant is a Risk Factor for Synucleinopathies: A Meta-Analysis.
medRxiv : the preprint server for health sciences, 2026
Main article
Open
GBA1 NM_000157.4:c.1279G>A Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with c.1223C>T; Thr369Met; Thr408Met
context: Compound heterozygous candidate
40671875
GBA genotype-Parkinson's phenotype correlation in a cohort of 252 Italian patients from the Tuscany region.
Clinical parkinsonism & related disorders, 2025
Main article
Open
GBA1 NM_000157.4:c.1495G>A Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with c.1226A > G; p.(Asn409Ser); p.N370S
context: Compound heterozygous candidate
40542290
Exploring GBA1 gene in Parkinson's disease: Prevalence and variant spectrum from Asia minor.
Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology, 2025
Main article
Open
GBA1 NM_000157.4:c.1495G>A Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with c.1226A>G; p.N409S
context: Compound heterozygous candidate
40137425
Clinical Outcomes and Genetic Mutations in Turkish Patients with Type 1 Gaucher Disease: Insights from a Single-Center Study.
Journal of personalized medicine, 2025
Main article
Open
GBA1 NM_000157.4:c.535G>C Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with c.1093G>A; E326K; Glu365Lys
context: Compound heterozygous candidate
36598340
Classification of GBA1 Variants in Parkinson's Disease: The GBA1-PD Browser.
Movement disorders : official journal of the Movement Disorder Society, 2023
Main article
Open
GBA1 NM_000157.4:c.535G>C Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with c.1093G > A; E326K; Glu365Lys
context: Compound heterozygous candidate
33420335
False negatives in GBA1 sequencing due to polymerase dependent allelic imbalance.
Scientific reports, 2021
Main article
Open
GBA1 NM_000157.4:c.1103G>A Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with p.Asn409Ser; p.Leu483Pro
context: Compound heterozygous candidate
33473340
Genetic characterization of the Albanian Gaucher disease patient population.
JIMD reports, 2020
Supplementary material
Open
GBA1 NM_000157.4:c.902G>A Phase-unconfirmed biallelic evidence
Needs review
Homozygous for query variant
context: Homozygous evidence
32714263
Association Between Glucocerebrosidase Mutations and Parkinson's Disease in Ireland.
Frontiers in neurology, 2020
Main article
Open
GBA1 NM_000157.4:c.535G>C Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with c.1093G > A; c.1226A > G; c.1604G > A; +6 more
context: Compound heterozygous candidate
32618053
A Large-Scale Full GBA1 Gene Screening in Parkinson's Disease in the Netherlands.
Movement disorders : official journal of the Movement Disorder Society, 2020
Main article
Open
GBA1 NM_000157.4:c.637C>T Phase-unconfirmed biallelic evidence
Needs review
Possible compound heterozygous with c.1226A > G; N370S; p.N409S
context: Compound heterozygous candidate
32547927
Gaucher disease: Biochemical and molecular findings in 141 patients diagnosed in Greece.
Molecular genetics and metabolism reports, 2020
Main article
Open
GBA1 NM_000157.4:c.535G>C Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with c.1093G>A; c.1223C>T; p.Glu365Lys; +1 more
context: Compound heterozygous candidate
29948939
Characterization of Brain Lysosomal Activities in GBA-Related and Sporadic Parkinson's Disease and Dementia with Lewy Bodies.
Molecular neurobiology, 2019
Supplementary material
Open
GBA1 NM_000157.4:c.1200G>A Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with G202R; G241R
context: Compound heterozygous candidate
29980418
Alleles with more than one mutation can complicate genotype/phenotype studies in Mendelian disorders: Lessons from Gaucher disease.
Molecular genetics and metabolism, 2018
Main article
Open
GBA1 NM_000157.4:c.1495G>A Phase-unconfirmed biallelic evidence
High confidence
Homozygous for query variant
context: Homozygous evidence
29124790
Neuropathology of genetic synucleinopathies with parkinsonism: Review of the literature.
Movement disorders : official journal of the Movement Disorder Society, 2017
Main article
Open
GBA1 NM_000157.4:c.1474G>A Phase-unconfirmed biallelic evidence
High confidence
Potential PM3 evidence identified; genotype context not structured
context: Compound heterozygous candidate
26296077
GBA Variants are associated with a distinct pattern of cognitive deficits in Parkinson's disease.
Movement disorders : official journal of the Movement Disorder Society, 2016
Main article
Open
GBA1 NM_000157.4:c.637C>T Phase-unconfirmed biallelic evidence
Needs review
Possible compound heterozygous with N370S
context: Compound heterozygous candidate
23430543
Novel mutations in the glucocerebrosidase gene of brazilian patients with Gaucher disease.
JIMD reports, 2013
Main article
Open
GBA1 NM_000157.4:c.535G>C Phase-unconfirmed biallelic evidence
High confidence
Possible compound heterozygous with c.10936G>A; c.586A>C; p.Glu326Lys; +1 more
context: Compound heterozygous candidate
21796727
A mutation in SCARB2 is a modifier in Gaucher disease.
Human mutation, 2011
Main article
Open
GBA1 NM_000157.4:c.1279G>A No PM3 Evidence Identified
Not assessed
No PM3 candidate genotype identified 41519835
Metabolomic breath landscape analysis unravels lipid biomarker candidates in patients with genetic and idiopathic Parkinson's disease.
NPJ Parkinson's disease, 2026
Main article
Open
GBA1 NM_000157.4:c.535G>C No PM3 Evidence Identified
Not assessed
No PM3 candidate genotype identified 41519835
Metabolomic breath landscape analysis unravels lipid biomarker candidates in patients with genetic and idiopathic Parkinson's disease.
NPJ Parkinson's disease, 2026
Main article
Open
GBA1 NM_000157.4:c.535G>C No PM3 Evidence Identified
Not assessed
No PM3 candidate genotype identified 41413081
The genetic architecture of Parkinson's disease on the Island of Crete.
NPJ Parkinson's disease, 2025
Main article
Open
GBA1 NM_000157.4:c.1279G>A No PM3 Evidence Identified
Not assessed
No PM3 candidate genotype identified 40506446
Penetrance of Parkinson's disease in GBA1 carriers depends on variant severity and polygenic background.
NPJ Parkinson's disease, 2025
Main article
Open